Editing Pediatrics: Prune-Belly Syndrome (section)

=== Extra-genitourinary Abnormalities ===

# '''<span style="color:#ff0000">Abdominal Wall Defect'''
#* The inferior and medial segments are the most consistently affected
# '''<span style="color:#ff0000">Cardiac Anomalies'''
## '''Patent ductus arteriosus'''
## '''Atrial septal defect'''
## '''Ventricular septal defect'''
## '''Tetralogy of Fallot'''
# '''<span style="color:#ff0000">Pulmonary'''
#* '''Pulmonary hypoplasia'''
#** Can result from severe oligohydramnios related to renal dysplasia or severe bladder outlet obstruction
#* '''Pneumomediastinum'''
#* '''Pneumothorax'''
#* '''Pneumonia and lobar atelectasis'''
# '''<span style="color:#ff0000">Gastrointestinal abnormalities'''
#* '''Increased bowel mobility with intestinal malrotation, volvulus, atresias, and stenosis'''

* It is exceptionally rare to encounter a normal urinary tract in association with the characteristic abdominal wall defect in a male. However, the converse is not unusual. Some patients (with pseudo-prune-belly syndrome) with a normal or relatively normal abdominal wall exhibit many or all of the internal urologic features. These features may include dysplastic or dysmorphic kidneys or dilated and tortuous ureters