Disorders of Sexual Differentiation: Difference between revisions

Line 736: Line 736:
***'''In addition to defining müllerian anatomy and confirming the presence or absence of a uterus, the gonads and adrenals should be studied.'''
***'''In addition to defining müllerian anatomy and confirming the presence or absence of a uterus, the gonads and adrenals should be studied.'''


==== '''Labs''' ====
==== Labs ====
*'''Karyotype'''  
*'''Karyotype'''  
**Should be obtained within the immediate neonatal period
**Should be obtained within the immediate neonatal period
Line 753: Line 753:
**May define the precise genetic abnormality responsible for a given DSD, be it abnormal androgen receptor or an enzyme abnormality.
**May define the precise genetic abnormality responsible for a given DSD, be it abnormal androgen receptor or an enzyme abnormality.


==== '''Imaging''' ====
==== Imaging ====
*'''Pelvis US to determine presence of Mullerian-derived structures'''
*'''Pelvis US to determine presence of Mullerian-derived structures'''
*'''Laparotomy or laparoscopy in this setting remains a diagnostic maneuver'''; removal of gonads or reproductive organs should be deferred until the final pathology report is available and a gender has been assigned.
*'''Laparotomy or laparoscopy in this setting remains a diagnostic maneuver'''; removal of gonads or reproductive organs should be deferred until the final pathology report is available and a gender has been assigned.